JPOSNA May 2021: Skeletal Dysplasia Quiz
{"name":"JPOSNA May 2021: Skeletal Dysplasia Quiz", "url":"https://www.quiz-maker.com/Q402X2C6C","txt":"This Skeletal Dysplasia Quiz represents an interactive session where POSNA members are able to work through 9 clinical scenarios to challenge how they would address these problems. Associated with each scenario is an OITE-style question and multiple choice options that seek the most preferred answer. In addition to the answer and follow-up radiographs, we have enlisted the opinions of POSNA experts in skeletal dysplasia to provide an evidenced-based approach to thinking through each problem. Quiz Authors: William G. Mackenzie, MD Department of Orthopaedics, Nemours\/A I duPont Hospital for Children, Wilmington, DE Klane K. White, MD, MScSeattle Children’s Hospital, University of Washington School of Medicine, Seattle, WA Matt Bernstein, MDPortland Shrine Hospital for Children, Portland, OR Samantha Spencer, MDBoston Children’s Hospital, Boston, MA, A four-month-old child with achondroplasia presents with a history of limited upper and lower extremity movements and hypotonia. His parents report that he has had several incidences of apnea while in the car seat. On physical exam, his head circumference is at the 90th percentile for achondroplasia. There are typical features of achondroplasia and the neurological exam suggests extremity weakness. What is the next best step for this patient?, A fourteen-year-old young man with achondroplasia presents with progressive thoracolumbar kyphosis. He complains of pain over his back deformity and limited walking endurance. His attempts to walk long distances results in tingling and weakness in his lower extremities. There is weakness of ankle dorsiflexion and hyperreflexia. Spine x-rays and MRI were obtained as seen below. What should be done at this point?","img":"https://www.quiz-maker.com/3012/images/ogquiz.png"}